Abstract: Objective:To sum perioperative management experiences of congenital heart diseases with diminutive pulmonary blood.Methods:The data of 233 cases with congenital heart diseases with diminutive pulmonary blood were analyzed retrospectively.The appropriate surgical programme was formulated after the diagnosis was confirmed by cardiac echocardiography,magnetic resonance imaging or spiral CT and pulmonary vessels were evaluated.Two hundred and one cases were treated with anatomical correction surgery and 34 cases were treated with physical or palliative surgery.All monitoring index of all cases were observed,and which were given full sedation,proper posture,circulation and respiratory support after opertaion.Results:The cardiopulmonary bypass time was(118.2327.25) minutes,aortic cross-clamping time 73.26 minutes,postoperative ventilation time(17.6412.23) minutes,average application amount of dopamine(7.522.12) mgkg-1min-1,intensive care time for(73.224.5) hours and postoperative hospital stay time(9.55.6) days.Eleven patients died(mortality as 73.3%) during intraoperative.Fifty-two patients had complications(incidence rate as 23.4%) and no one died.Conclusions:The objective and comprehensive assessment of preoperative imaging,the correct choice of operation and postoperative care and treatment can greatly improve the surgical effects,reduce the incidence of surgical complications and mortality.